Мультидисциплинарный подход к коррекции уремического синдрома у пациентки с ангиомиолипомой почки
Date
2017-06
Authors
Lisovyi, Volodymyr
Polyakov, Nikolay
Andonieva, Nina
Journal Title
Journal ISSN
Volume Title
Publisher
Abstract
Abstract
Patients with uremic syndrome are at high risk of developing various complications that can
lead to fatal consequences. Uremic syndrome usually develops on the background of chronic
kidney disease, especially its later stages. However, uremia may also occur as a result of tumor,
surgical treatment of which can lead the patient to renoprival state. According to various au-
thors, the development of uremic syndrome occurs in 7-10% of patients suffering from kidney
tumors.
Renal angiomyolipoma is a benign mesenchymal tumor, which accounts for 3% of all tumors
of renal parenchyma and 90% of all benign tumors of the kidney. It is known that angiomyoli-
poma is characterized by slow growth and the associated asymptomatic course.
Present study describes a case of uremic syndrome developed as a result of kidney angiomyo-
lipoma in a 32-year-old female patient, who earlier underwent nephrectomy in connection with
angiomyolipoma of the contralateral kidney. The computer tomography allowed to reveal a large
retroperitoneal space-occupying lesion and to detect a spontaneous rupture of this formation, in
connection with which the patient underwent a revision of the retroperitoneal space. While mak-
ing the revision of the tumor no kidney authentic tissues were clearly detected. That was the
reason for performing the nephrectomy. The patient has begun renal replacement therapy using
haemodialysis. The mother of the patient expressed a desire to become a kidney donor for the
daughter. As a result of examination in the potential donor a renal artery aneurism was revealed.
After examination of the donor and recipient, the patient has successfully undergone living-
related kidney transplantation, and the kidney donor – renal artery plasty.
Thus, the specialized urological management, haemodialysis as a method of renal replace-
ment therapy and the living-related kidney transplantation, concentrated in one center, have
given the chance to provide maximal rehabilitation of the patient with the uremic syndrome as
well as to prevent fatal complications in the kidney donor.
Description
Keywords
uremic syndrome, kidney angiomyolipoma, renal replacement therapy, living-related kidney transplantation
Citation
Lesovoy V. A multidisciplinary approach to the correction of uremic syndrome in a patient with kidney angiomyolipoma / Vladimir Lesovoy, Nikolay Polyakov, Nina Andonieva // The New Armenian Medical Journal. – 2017. – Vol. 11, Nо 2. – P. 6–9.